Occurrence of Lysoganglioside Lyso-GM2 (II3-Neu5Ac-Gangliotriaosylsphingosine) in GM2 Gangliosidosis Brain
S NEUENHOFER, E CONZELMANN… - 1986 - degruyter.com
S NEUENHOFER, E CONZELMANN, G SCHWARZMANN, H EGGE, K SANDHOFF
1986•degruyter.comLysoganglioside lyso-GM2 (sialyl- a concentration of approx. 15 nmol/g wet tissue,
gangliotriaosylsphingosine) was detected in a Neither lysoganglioside lyso-GM2 nor the
corbrain sample of a patient with variant B of in- responding GM1 derivative could be
detected in fantile GM2 gangliosidosis (Tay-Sachs disease) at normal brain.
gangliotriaosylsphingosine) was detected in a Neither lysoganglioside lyso-GM2 nor the
corbrain sample of a patient with variant B of in- responding GM1 derivative could be
detected in fantile GM2 gangliosidosis (Tay-Sachs disease) at normal brain.
Summary
Lysoganglioside lyso-GM2 (sialyl- a concentration of approx. 15 nmol/g wet tissue, gangliotriaosylsphingosine) was detected in a Neither lysoganglioside lyso-GM2 nor the corbrain sample of a patient with variant B of in- responding GM1 derivative could be detected in fantile GM2 gangliosidosis (Tay-Sachs disease) at normal brain.
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